Hutchinson- Gilford progeria syndrome is a very rare genetic disorder in children which causes accelerated aging involving bones, heart, skin and blood vessels. This condition is extremely rare, affecting only 1 in 4-8 million births.The features include premature aging, alopecia, cardiovascular problems, sclerodermatous skin changes and bone fragility. The main cause of death is Myocardial infarction, usually happens at an average age of 13 years. We are reporting a 2 year old boy showing features of this syndrome who was proven genetically as well.