Adenoid cystic carcinoma (AdCC) is a malignant salivary gland tumor with slow growth, but it has the potential for recurrence and distant metastasis. Metastasis to the kidney is very rarely reported.This study report a rare case of AdCC metastasis from the parotid gland to the left kidney with aim to provide clinical, radiological, and histopathological descriptions and emphasize the importance of differential diagnosis with primary renal cell carcinoma. A case study of a 42 year-old male patient with a left kidney mass who had a history of parotid AdCC one year earlier. Histopathological examination was performed after radical surgery. Histopathology showed a cribriform and lobulated pattern with epithelial and myoepithelial cell populations within a myxoid stroma, typical of AdCC. No perineural or vascular invasion was found. Although extremely rare, AdCC can metastasize to the kidney. Diagnosis requires comprehensive evaluation and a multidisciplinary approach.