Juvenile Myasthenia Gravis (JMG) is an uncommon autoimmune disorder characterized by muscle weakness and fatigue, with a prevalence of 10-15% among all myasthenia gravis cases. This report presents a rare case of JMG in a 4-year-old boy, detailing the clinical evaluation, diagnosis, and comprehensive management strategies. The patient exhibited bilateral ptosis and generalized muscle weakness, confirmed by elevated acetylcholine receptor antibodies and repetitive nerve stimulation tests. Management involved acetylcholinesterase inhibitors and corticosteroids, resulting in significant clinical improvement. Early diagnosis and a multidisciplinary approach are crucial for optimal outcomes in pediatric JMG cases.