Miller-Fischer Syndrome(MFS) is a less common variety of Guillain Barre Syndrome(GBS) having different incidences and is reported in all the age groups. Ataxia, areflexia and ophthalmoplegia are the cardinal features based on which the diagnosis is made. Anti-GQ1b antibody titres help in establishing the serological diagnosis. This case report is of a female child aged 4 years who was brought with progressive generalised weakness, lethargy, vomiting and double vision following a minor upper respiratory illness. The characteristic features of ataxia, areflexia, and ophthalmoplegia characteristic to MFS were present. The provisional diagnosis of MFS was proved by serology which showed anti-GQ1b antibodies positive and the child was managed with Intravenous immuno globulin (IVIG) following which the child improved.